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B6-hDMD (E44-45)
复苏/繁育服务
产品名称:
B6-hDMD (E44-45)
产品编号:
I001204
品系背景:
C57BL/6NCya
HUGO-GT®全基因组人源化模型
* 使用本品系发表的文献需注明:B6-hDMD (E44-45) mice (Catalog I001204) were purchased from Cyagen.
交付类型
周龄
性别
基因型
数量
品系描述
B6-hDMD (E44-45)小鼠是Dmd基因44-45号外显子人源化的模型,可用于杜氏肌营养不良症的研究。该模型的纯合子可存活且可育。此外,基于自主研发的TurboKnockout融合BAC重组技术,赛业生物还提供【hE49-53, del E50】、【hE49-53】、【hE44-45, del E44】、【hE44-45, c.6438+2 T to A】、【hE8-30】等人源化模型,覆盖大部分热门研究区域,并可根据不同突变需求提供定制服务。
相关疾病:
Muscular Dystrophy, Duchenne Type
Muscular Dystrophy, Becker Type
Cardiomyopathy, Dilated, 3b
Dystrophinopathies
Muscular Dystrophy
Duchenne and Becker Muscular Dystrophy
Muscular Atrophy
Symptomatic Form of Muscular Dystrophy of Duchenne and Becker in Female Carriers
Creatine Phosphokinase, Elevated Serum
Interatrial Communication
Isolated Elevated Serum Creatine Phosphokinase Levels
Atrial Heart Septal Defect
Myopathy
Beckwith-Wiedemann Syndrome
Familial Isolated Dilated Cardiomyopathy
Dilated Cardiomyopathy
Non-Syndromic X-Linked Intellectual Disability
Colorectal Cancer
Ptosis
Autism
Schizophrenia
应用领域
杜氏肌营养不良症(Duchenne muscular dystrophy,DMD)